Search Results for: kasabach-merritt syndrome

Histologic Diagnosis of Inflammatory Skin Diseases

Acroangiodermatitis of Mali/Stewart-Bluefarb syndrome

…Cause and mechanism The mechanisms that account for the changes in the skin in acroangiodermatitis and the Stewart-Bluefarb syndrome are not understood completely, but seem to be secondary to arteriovenous malformations, either congenital or…

Malignant cylindroma in a patient with Brooke-Spiegler syndrome

Malignant cylindroma in a patient with Brooke-Spiegler syndrome

…patients with multiple pre-existing benign lesions. Rare sporadic solitary tumors are also described [3,4]. Brooke-Spiegler syndrome (BSS) is the most frequently associated with malignant cylindromas. The syndrome has autosomal-dominant…

Histologic Diagnosis of Inflammatory Skin Diseases

Staphylococcal scalded skin syndrome

An inflammatory process expressed clinically by markedly edematous acuminate papules and edematous plaques situated mostly on the face, upper part of the trunk, and arms, especially the hands, and often accompanied by fever and leukocytosis. It may…

Histologic Diagnosis of Inflammatory Skin Diseases

Sweet’s syndrome

An inflammatory process expressed clinically by markedly edematous acuminate papules and edematous plaques situated mostly on the face, upper part of the trunk, and arms, especially the hands, and often accompanied by fever and leukocytosis. It may…

Histologic Diagnosis of Inflammatory Skin Diseases

Toxic shock syndrome

An inflammatory process expressed clinically by markedly edematous acuminate papules and edematous plaques situated mostly on the face, upper part of the trunk, and arms, especially the hands, and often accompanied by fever and leukocytosis. It may…

Histologic Diagnosis of Inflammatory Skin Diseases

Acroangiodermatitis of Mali/Stewart-Bluefarb syndrome

An inflammatory process expressed clinically by markedly edematous acuminate papules and edematous plaques situated mostly on the face, upper part of the trunk, and arms, especially the hands, and often accompanied by fever and leukocytosis. It may…

Histologic Diagnosis of Inflammatory Skin Diseases

Behçet’s Disease

…lberg, 1908. Braun-Falco O, Luderschmidt C, Wolff HH. The sterile Behçet pustule: a typical skin manifestation of the Behçet syndrome. Dtsch Med Wochenschr 1983;108:820-25. Chamberlain MA. A family study of Behçet’s syndrome. Ann Rheum Dis…

Histologic Diagnosis of Inflammatory Skin Diseases

Errors and Reasons

…matosis of Churg and Strauss, pustular bacterid of Andrews, the idiopathic atrophoderma of Pasini and Pierini, Lyell’s syndrome, Wells’ syndrome, etc., etc., etc. Error: “Germinal centers” in a nodular infiltrate composed…

Resolving Quandaries in Dermatology, Pathology & Dermatopathology

Churg-Strauss Granuloma and Allergic Granulomatosis?

…ding of the granulomatous lesions, both within vessel walls and in connective tissue throughout the body, suggests that this syndrome constitutes an entity apart from classical periarteritis nodosa. . . . Of frequent occurrence in this syndrome are…